Hypohidrotic Ectodermal Dysplasia with total anodontia: a case report

摘要

Ectodermal dysplasia is a hereditary disorder that occurs as a consequence of disturbances inthe ectoderm of the developing embryo. The triad of nail dystrophy, alopecia or hypotrichosis and palmoplantar hyperkeratosis is usually accompanied by a lack of sweat glands and a partial or complete absence of primary and/or permanent dentition. A case report illustrating the prosthetic rehabilitation of a seven year old boy with hypohidrotic ectodermal dysplasia associated with total anodontia is presented.